GLB1 (Beta-galactosidase, Beta-gal, Acid beta Galactosidase, Beta Galactosidase 1, Beta-galactosidase, EBP, ELNR1, Galactosidase beta 1, MPS4B) (Chimeric)

Catalogue Number: 361613-USB

Manufacturer:United States Biological
Physical state:Supplied as a liquid in PBS, pH 7.2, 0.02% Proclin-300.
Type:Monoclonal Primary Antibody - Unconjugated
Alias:acid beta-galactosidase|beta-galactosidase|EBP|elastin receptor 1, 67kDa|ELNR1|lactase|MPS4B
Shipping Condition:Blue Ice
Unit(s): 200 ug
Host name: Hamster
Clone: 13R4 (recomb)
Isotype: IgG
Immunogen: Beta-galactosidase.
Application: FC, WB

Description

Description: Recombinant monoclonal antibody to beta-galactosidase with variable regions (i.e., specificity) from scFv 13R4. This is a chimeric hamster antibody, created as part of a panel offering of antibodies of the same clone in different formats (species, isotype, subtype and modified versions). Manufactured using a proprietary recombinant platform technology. This gene encodes beta-galactosidase-1, a lysosomal enzyme that hydrolyzes the terminal beta-galactose from ganglioside substrates and other glycoconjugates. Defects in this gene are the cause of GM1-gangliosidosis and Morquio B syndrome. Multiple transcript variants encoding different isoforms have been found for this gene.

Additional Text

Gene Name

GLB1

Gene ID

2720

Uniprot ID

P16278

Specificity

Recognizes wild-type E. coli beta-galactosidase.

Purification

Protein A purified

Antibody Clonality

Recombinant Monoclonal