PEX26 antibody, Internal

Catalogue Number: GTX88069-GTX

Manufacturer:GeneTex
Preservative:0.02% Sodium azide
Physical state:Liquid
Type:Polyclonal Primary Antibody - Unconjugated
Alias:peroxisomal biogenesis factor 26 , PBD7A , PBD7B , PEX26M1T , Pex26pM1T
Shipping Condition:Blue Ice
Unit(s): 100 ug
Host name: Goat
Clone:
Isotype: IgG
Immunogen: Peptide with sequence C-QKPNLEGSVSHK, from the internal region of the protein sequence according to NP_060399.1.
Application: WB

Description

Description: This gene belongs to the peroxin-26 gene family. It is probably required for protein import into peroxisomes. It anchors PEX1 and PEX6 to peroxisome membranes, possibly to form heteromeric AAA ATPase complexes required for the import of proteins into peroxisomes. Defects in this gene are the cause of peroxisome biogenesis disorder complementation group 8 (PBD-CG8). PBD refers to a group of peroxisomal disorders arising from a failure of protein import into the peroxisomal membrane or matrix. The PBD group is comprised of four disorders: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP). Alternatively spliced transcript variants have been identified for this gene. [provided by RefSeq, Dec 2010]

Additional Text

Concentration

0.5 mg/ml

Gene Name

PEX26

Uniprot ID

Q7Z412

Gene ID

55670

Purification

Ammonium Sulfate Precipitated; Affinity Purified

Antibody Clonality

Polyclonal

Note

For In vitro laboratory use only. Not for any clinical, therapeutic, or diagnostic use in humans or animals. Not for animal or human consumption

Molecular Weight

34

Application Notes

WB: 0.5-1.5µg/ml. *Optimal dilutions/concentrations should be determined by the researcher.Not tested in other applications.